FETAL RHABDOMYOMA OF THE HEAD AND NECK: CLINICOPATHOLOGIC AND IMMUNOPHENOTYPIC STUDY OF 24 CASES (Kapadia et al. Hum Pathol 24: 754-765, 1993).
Twenty four fetal rhabdomyomas (FRM): 16 males, 7 females.
Age: Median 4.5 years (3 days to 58 yrs.), 42% younger than 1 yr., 46% older than 15 yrs., 25% congenital.
Only one patient with local recurrence.
Pathologic features: 8 cases of classic FRM, 16 cases of intermediate FRM.
No mitosis in 19 cases; in 5: 1 to 14/50 HPF.
Marked nuclear atypia, anaplasia, “cambium layer”: Absent.
IH: Pos. for myoglobin, desmin, MSA. Neg. for CK, EMA, CD68.