PLEUROPULMONARY BLASTOMA. THE SO-CALLED PULMONARY BLASTOMA OF CHILDHOOD (Manivel et al. Cancer 62: 1516-1526, 1988).
Eleven pediatric intrathoracic neoplasms.
Intrapulmonary, mediastinal or pleural-based masses.
Small. primitive cells with blastomatous qualities, uncommitted stroma.
Focal rhabdomyosarcomatous, chondrosarcomatous, and liposarcomatous differentiation.
No malignant epithelial component.
Different from pulmonary blastoma in adults; designation of pleuropulmonary blastoma is suggested.